Posterior reversible encephalopathy syndrome following immunoglobulin therapy in a patient with Miller-Fisher syndrome

نویسندگان

  • Bruno Niemeyer de Freitas Ribeiro
  • Tiago Medina Salata
  • Rafael Silveira Borges
  • Edson Marchiori
چکیده

Radiol Bras. 2016 Jan/Fev;49(1):56–64 58 http://dx.doi.org/10.1590/0100-3984.2014.0057 infarction, spontaneous or traumatic rupture, congestive heart failure, and Kasabach-Merritt syndrome. A correct diagnosis of the pedunculated lesion may be difficult, despite the typical radiological presentation, because of the limitation in define the origin of the mass, since a thin pedicle may be almost undetectable at images. The most used modalities of imaging in diagnosis include US, CT and MRI. At US, the image is typically hyperechoic, homogeneous, with well defined margins; and, in cases of giant lesions, central heterogeneity may be present. At CT, with a certain frequency, giant hemangiomas do not present with the typical pattern of hypoattenuating lesion with centripetal enhancement and homogenization at delayed sections, due to the presence of avascular areas of necrosis, fibrosis or hemorrhage. MRI is the most sensitive and specific (> 90%) diagnostic method. The lesions are well defined, homogeneous, with low signal intensity at T1-weighted sequences, and high signal intensity at T2-weighted sequences. Biopsy is not recommended in such cases, due to the risk of hemorrhage. There are reports in the literature describing pedunculated hemangiomas as gastric, adrenal tumor, retroperitoneal mass, other pedunculated liver tumors such as hepatocellular carcinoma, mesenchymal hamartoma, focal nodular hyperplasia or adenoma. Surgical treatment is reserved for cases of giant or symptomatic lesions, uncertain diagnosis, lesions with complications, and for cases of pedunculated hemangiomas due to their tendency to torsion. REFERENCES

برای دانلود متن کامل این مقاله و بیش از 32 میلیون مقاله دیگر ابتدا ثبت نام کنید

ثبت نام

اگر عضو سایت هستید لطفا وارد حساب کاربری خود شوید

منابع مشابه

Unexpected Maternal Convulsion: An Idiopathic Case of Posterior Reversible Encephalopathy Syndrome after Delivery

Posterior reversible encephalopathy syndrome (PRES) is associated with various clinical manifestations such as headache, blurred vision, confusion and tonic-clonic convulsion. Some of the predisposing factors for PRES include hypertensive encephalopathy, preeclampsia and eclampsia, lupus erythematosus, thrombotic thrombocytopenic purpura and long-term use of immunosuppressive drugs. This condit...

متن کامل

Posterior reversible Leukoencephalopathy following thrombotic thrombocytopenic purpura at postpartum period: case report

Background: Posterior reversible leukoencephalopathy syndrome (PRLS) is a clinical and radiological syndrome of heterogeneous etiologies that are grouped because of the similar findings on neuroimaging studies which may occur at any age. The pathogenesis of RPLS remains unclear, but it appears to be related to disordered cerebral autoregulation and endothelial dysfunction. The syndrome is more ...

متن کامل

Posterior reversible encephalopathy syndrome in a patient with mixed connective tissue disease: a case report

BACKGROUND Posterior reversible encephalopathy is a syndrome highly associated with hypertension and cytotoxic therapy. The syndrome typically presents with headache, visual abnormality, seizures and characteristic vasogenic edema on magnetic resonance imaging. The entity warrants a prompt diagnosis to avoid deteriorating consequences. CASE PRESENTATION In this report, we describe a 15-year-o...

متن کامل

Intestinal perforation: an unusual complication of barium enema

1. Hospital Casa de Portugal, Rio de Janeiro, RJ, Brazil. 2. Instituto Estadual do Cérebro Paulo Niemeyer, Rio de Janeiro, RJ, Brazil. Mailing address: Dr. Tiago Medina Salata. Rua do Bispo, 72, Rio Comprido. Rio de Janeiro. RJ, Brazil, 20261-064. E-mail: [email protected]. imaging with absence of typical movement disorder symptoms (hemichorea-hemiballism). J Radiol Case Rep. 2013;7:1–9...

متن کامل

Systemic Lupus Erythematosus Presenting With Posterior Reversible Encephalopathy Syndrome: An Unusual Case

Posterior reversible encephalopathy syndrome (PRES) has been reported in association with hypertension, renal failure, transplantation and immunosuppressives [1]. However, reports of PRES in conjunction with SLE are sparse [2]. Majority of these patients had lupus nephritis and hypertension [3]. Recent reports have shown a stringent association of PRES with hypertension in SLE patients and resp...

متن کامل

ذخیره در منابع من


  با ذخیره ی این منبع در منابع من، دسترسی به آن را برای استفاده های بعدی آسان تر کنید

برای دانلود متن کامل این مقاله و بیش از 32 میلیون مقاله دیگر ابتدا ثبت نام کنید

ثبت نام

اگر عضو سایت هستید لطفا وارد حساب کاربری خود شوید

عنوان ژورنال:

دوره 49  شماره 

صفحات  -

تاریخ انتشار 2016